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Defective fluid transport by cystic fibrosis airway epithelia.

Cystic fibrosis (CF) airway epithelia exhibit defective transepithelial electrolyte transport: cAMP-stimulated Cl- secretion is abolished because of the loss of apical membrane cystic fibrosis transmembrane conductance regulator (CFTR) Cl- channels, and amiloride-sensitive Na+ absorption is increase...

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Autors principals: Smith, J J, Karp, P H, Welsh, M J
Format: Artigo
Idioma:Inglês
Publicat: 1994
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC294089/
https://ncbi.nlm.nih.gov/pubmed/8132771
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