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Mutant superoxide dismutase 1-induced IL-1β accelerates ALS pathogenesis

ALS is a fatal motor neuron disease of adult onset. Neuroinflammation contributes to ALS disease progression; however, the inflammatory trigger remains unclear. We report that ALS–linked mutant superoxide dismutase 1 (SOD1) activates caspase-1 and IL-1β in microglia. Cytoplasmic accumulation of muta...

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Autors principals: Meissner, Felix, Molawi, Kaaweh, Zychlinsky, Arturo
Format: Artigo
Idioma:Inglês
Publicat: National Academy of Sciences 2010
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2919927/
https://ncbi.nlm.nih.gov/pubmed/20616033
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1002396107
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