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Biphasic Myopathic Phenotype of Mouse DUX, an ORF within Conserved FSHD-Related Repeats

Facioscapulohumeral muscular dystrophy (FSHD) is caused by contractions of D4Z4 repeats at 4q35.2 thought to induce misregulation of nearby genes, one of which, DUX4, is actually localized within each repeat. A conserved ORF (mDUX), embedded within D4Z4-like repeats, encoding a double-homeodomain pr...

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Bibliografski detalji
Glavni autori: Bosnakovski, Darko, Daughters, Randy S., Xu, Zhaohui, Slack, Jonathan M. W., Kyba, Michael
Format: Artigo
Jezik:Inglês
Izdano: Public Library of Science 2009
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC2737622/
https://ncbi.nlm.nih.gov/pubmed/19756142
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0007003
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