Caricamento...

Temperature sensitivity of human perforin mutants unmasks subtotal loss of cytotoxicity, delayed FHL, and a predisposition to cancer

The pore-forming protein perforin is critical for defense against many human pathogens and for preventing a catastrophic collapse of immune homeostasis, manifested in infancy as Type 2 familial hemophagocytic lymphohistiocytosis (FHL). However, no evidence has yet linked defective perforin cytotoxic...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Autori principali: Chia, Jenny, Yeo, Kim Pin, Whisstock, James C., Dunstone, Michelle A., Trapani, Joseph A., Voskoboinik, Ilia
Natura: Artigo
Lingua:Inglês
Pubblicazione: National Academy of Sciences 2009
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2701033/
https://ncbi.nlm.nih.gov/pubmed/19487666
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0903815106
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !