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Noninvasive Measurement of Protein Aggregation by Mutant Huntingtin Fragments or α-Synuclein in the Lens

Many diverse human diseases are associated with protein aggregation in ordered fibrillar structures called amyloid. Amyloid formation may mediate aberrant protein interactions that culminate in neurodegeneration in Alzheimer, Huntington, and Parkinson diseases and in prion encephalopathies. Studies...

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Autores principales: Muchowski, Paul J., Ramsden, Richard, Nguyen, QuangVu, Arnett, Ernest E., Greiling, Teri M., Anderson, Susan K., Clark, John I.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2007
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2650484/
https://ncbi.nlm.nih.gov/pubmed/18167346
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M709678200
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