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Requirement of an intact microtubule cytoskeleton for aggregation and inclusion body formation by a mutant huntingtin fragment

Huntington's disease is caused by the expansion of CAG repeats coding for a polyglutamine tract in the huntingtin protein. The major pathological feature found in Huntington's disease neurons is the presence of detergent-insoluble ubiquitinated inclusion bodies composed of the huntingtin p...

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Autors principals: Muchowski, Paul J., Ning, Ke, D'Souza-Schorey, Crislyn, Fields, Stanley
Format: Artigo
Idioma:Inglês
Publicat: The National Academy of Sciences 2002
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC117373/
https://ncbi.nlm.nih.gov/pubmed/11792857
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.022628699
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