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Increased expression of urokinase plasminogen activator in Quebec platelet disorder is linked to megakaryocyte differentiation

Quebec platelet disorder (QPD) is an inherited bleeding disorder associated with increased urokinase plasminogen activator (uPA) in platelets but not in plasma, intraplatelet plasmin generation, and α-granule protein degradation. These abnormalities led us to investigate uPA expression by QPD CD34(+...

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Main Authors: Veljkovic, D. Kika, Rivard, Georges E., Diamandis, Maria, Blavignac, Jessica, Cramer-Bordé, Elisabeth M., Hayward, Catherine P. M.
格式: Artigo
語言:Inglês
出版: American Society of Hematology 2009
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在線閱讀:https://ncbi.nlm.nih.gov/pmc/articles/PMC2644081/
https://ncbi.nlm.nih.gov/pubmed/19029443
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/blood-2008-08-172338
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