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Out of breath: GM-CSFRα mutations disrupt surfactant homeostasis

Pulmonary alveolar proteinosis (PAP) is a rare disorder in which surfactant homeostasis in the lung is impaired, causing respiratory distress and, in severe cases, respiratory failure. Most cases of PAP are associated with the formation of autoantibodies against the cytokine granulocyte/macrophage c...

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Autors principals: Notarangelo, Luigi D., Pessach, Itai
Format: Artigo
Idioma:Inglês
Publicat: The Rockefeller University Press 2008
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2585835/
https://ncbi.nlm.nih.gov/pubmed/19015311
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1084/jem.20082378
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