Out of breath: GM-CSFRα mutations disrupt surfactant homeostasis

Pulmonary alveolar proteinosis (PAP) is a rare disorder in which surfactant homeostasis in the lung is impaired, causing respiratory distress and, in severe cases, respiratory failure. Most cases of PAP are associated with the formation of autoantibodies against the cytokine granulocyte/macrophage c...

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Bibliografiska uppgifter
Huvudupphovsmän: Notarangelo, Luigi D., Pessach, Itai
Materialtyp: Artigo
Språk:Inglês
Publicerad: The Rockefeller University Press 2008
Ämnen:
Commentaries
Länkar:https://ncbi.nlm.nih.gov/pmc/articles/PMC2585835/
https://ncbi.nlm.nih.gov/pubmed/19015311
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1084/jem.20082378
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