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Activation of the Unfolded Protein Response by ΔF508 CFTR

Environmental insults and misfolded proteins cause endoplasmic reticulum (ER) stress and activate the unfolded protein response (UPR). The UPR decreases endogenous cystic fibrosis transmembrane conductance regulator (CFTR) mRNA levels and protein maturation efficiency. Herein, we investigated the ef...

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Detaylı Bibliyografya
Asıl Yazarlar: Bartoszewski, Rafal, Rab, Andras, Jurkuvenaite, Asta, Mazur, Marina, Wakefield, John, Collawn, James F., Bebők, Zsuzsa
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: American Thoracic Society 2008
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC2551705/
https://ncbi.nlm.nih.gov/pubmed/18458236
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1165/rcmb.2008-0065OC
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