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Mechanisms of cardiac arrhythmias and sudden death in transgenic rabbits with long QT syndrome

Long QT syndrome (LQTS) is a heritable disease associated with ECG QT interval prolongation, ventricular tachycardia, and sudden cardiac death in young patients. Among genotyped individuals, mutations in genes encoding repolarizing K(+) channels (LQT1:KCNQ1; LQT2:KCNH2) are present in approximately...

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Main Authors: Brunner, Michael, Peng, Xuwen, Liu, Gong Xin, Ren, Xiao-Qin, Ziv, Ohad, Choi, Bum-Rak, Mathur, Rajesh, Hajjiri, Mohammed, Odening, Katja E., Steinberg, Eric, Folco, Eduardo J., Pringa, Ekatherini, Centracchio, Jason, Macharzina, Roland R., Donahay, Tammy, Schofield, Lorraine, Rana, Naveed, Kirk, Malcolm, Mitchell, Gary F., Poppas, Athena, Zehender, Manfred, Koren, Gideon
פורמט: Artigo
שפה:Inglês
יצא לאור: American Society for Clinical Investigation 2008
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גישה מקוונת:https://ncbi.nlm.nih.gov/pmc/articles/PMC2373420/
https://ncbi.nlm.nih.gov/pubmed/18464931
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI33578
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