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Mechanisms of cardiac arrhythmias and sudden death in transgenic rabbits with long QT syndrome

Long QT syndrome (LQTS) is a heritable disease associated with ECG QT interval prolongation, ventricular tachycardia, and sudden cardiac death in young patients. Among genotyped individuals, mutations in genes encoding repolarizing K(+) channels (LQT1:KCNQ1; LQT2:KCNH2) are present in approximately...

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Bibliografische gegevens
Hoofdauteurs: Brunner, Michael, Peng, Xuwen, Liu, Gong Xin, Ren, Xiao-Qin, Ziv, Ohad, Choi, Bum-Rak, Mathur, Rajesh, Hajjiri, Mohammed, Odening, Katja E., Steinberg, Eric, Folco, Eduardo J., Pringa, Ekatherini, Centracchio, Jason, Macharzina, Roland R., Donahay, Tammy, Schofield, Lorraine, Rana, Naveed, Kirk, Malcolm, Mitchell, Gary F., Poppas, Athena, Zehender, Manfred, Koren, Gideon
Formaat: Artigo
Taal:Inglês
Gepubliceerd in: American Society for Clinical Investigation 2008
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Online toegang:https://ncbi.nlm.nih.gov/pmc/articles/PMC2373420/
https://ncbi.nlm.nih.gov/pubmed/18464931
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI33578
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