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Wobble modification defect in tRNA disturbs codon–anticodon interaction in a mitochondrial disease

We previously showed that in mitochondrial tRNA(Lys) with an A8344G mutation responsible for myoclonus epilepsy associated with ragged-red fibers (MERRF), a subgroup of mitochondrial encephalomyopathic diseases, the normally modified wobble base (a 2-thiouridine derivative) remains unmodified. Since...

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Autori principali: Yasukawa, Takehiro, Suzuki, Tsutomu, Ishii, Norie, Ohta, Shigeo, Watanabe, Kimitsuna
Natura: Artigo
Lingua:Inglês
Pubblicazione: Oxford University Press 2001
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC125593/
https://ncbi.nlm.nih.gov/pubmed/11532943
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/emboj/20.17.4794
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