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CAG repeat instability in embryonic stem cells and derivative spermatogenic cells of transgenic Huntington’s disease monkey

PURPOSE: The expansion of CAG (glutamine; Q) trinucleotide repeats (TNRs) predominantly occurs through male lineage in Huntington’s disease (HD). As a result, offspring will have larger CAG repeats compared to their fathers, which causes an earlier onset of the disease called genetic anticipation. T...

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Publicado en:J Assist Reprod Genet
Autores principales: Khampang, Sujittra, Parnpai, Rangsun, Mahikul, Wiriya, Easley, Charles A., Cho, In Ki, Chan, Anthony W.S.
Formato: Artigo
Lenguaje:Inglês
Publicado: Springer US 2021
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC8190423/
https://ncbi.nlm.nih.gov/pubmed/33611676
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10815-021-02106-3
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