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A Niemann‐pick C1 disease child with BCG-itis: a case report and analysis

BACKGROUND: Niemann-Pick C disease is a rare autosomal recessive lysosomal lipid storage disorder. Some primary immunodeficiency diseases patients developed regional disease or disseminated disease after vaccinating BCG. It is unclear whether NPC gene deficiency is associated with Mycobacteria infec...

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Detalhes bibliográficos
Publicado no:BMC Pediatr
Main Authors: Lin, Jing-jing, Liu, Xu-hui, Xia, Lu, Feng, Yan-ling, Xi, Xiu-hong, Lu, Shui-hua
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2021
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC8094597/
https://ncbi.nlm.nih.gov/pubmed/33947371
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12887-021-02671-7
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