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A Niemann‐pick C1 disease child with BCG-itis: a case report and analysis

BACKGROUND: Niemann-Pick C disease is a rare autosomal recessive lysosomal lipid storage disorder. Some primary immunodeficiency diseases patients developed regional disease or disseminated disease after vaccinating BCG. It is unclear whether NPC gene deficiency is associated with Mycobacteria infec...

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Detalles Bibliográficos
Publicado en:BMC Pediatr
Main Authors: Lin, Jing-jing, Liu, Xu-hui, Xia, Lu, Feng, Yan-ling, Xi, Xiu-hong, Lu, Shui-hua
Formato: Artigo
Idioma:Inglês
Publicado: BioMed Central 2021
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC8094597/
https://ncbi.nlm.nih.gov/pubmed/33947371
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12887-021-02671-7
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