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Therapeutic efficacy of antisense oligonucleotides in mouse models of CLN3 Batten disease

CLN3 Batten disease is an autosomal recessive, neurodegenerative, lysosomal storage disease caused by mutations in CLN3, which encodes a lysosomal membrane protein(1–3). There are no disease-modifying treatments for this disease that affects up to 1 in 25,000 births, has an onset of symptoms in earl...

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Publicado en:Nat Med
Main Authors: Centa, Jessica L., Jodelka, Francine M., Hinrich, Anthony J., Johnson, Tyler B., Ochaba, Joseph, Jackson, Michaela, Duelli, Dominik M., Weimer, Jill M., Rigo, Frank, Hastings, Michelle L.
Formato: Artigo
Idioma:Inglês
Publicado: 2020
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC8008709/
https://ncbi.nlm.nih.gov/pubmed/32719489
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41591-020-0986-1
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