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Assessment of Distinct Electrophysiological Parameters in Rectal Biopsies for the Choice of the Best Diagnosis/Prognosis Biomarkers for Cystic Fibrosis

Most cases of Cystic Fibrosis (CF) are diagnosed early in life. However, people with atypical CF forms pose diagnosis dilemmas, requiring laboratory support for diagnosis confirmation/exclusion. Ex vivo analysis of fresh rectal biopsies by Ussing chamber has been the best discriminant biomarker for...

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Publicat a:Front Physiol
Autors principals: Silva, Iris A. L., Duarte, Aires, Marson, Fernando A. L., Centeio, Raquel, Doušová, Tereza, Kunzelmann, Karl, Amaral, Margarida D.
Format: Artigo
Idioma:Inglês
Publicat: Frontiers Media S.A. 2020
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7786280/
https://ncbi.nlm.nih.gov/pubmed/33424627
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fphys.2020.604580
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