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Assessment of Distinct Electrophysiological Parameters in Rectal Biopsies for the Choice of the Best Diagnosis/Prognosis Biomarkers for Cystic Fibrosis

Most cases of Cystic Fibrosis (CF) are diagnosed early in life. However, people with atypical CF forms pose diagnosis dilemmas, requiring laboratory support for diagnosis confirmation/exclusion. Ex vivo analysis of fresh rectal biopsies by Ussing chamber has been the best discriminant biomarker for...

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Pubblicato in:Front Physiol
Autori principali: Silva, Iris A. L., Duarte, Aires, Marson, Fernando A. L., Centeio, Raquel, Doušová, Tereza, Kunzelmann, Karl, Amaral, Margarida D.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7786280/
https://ncbi.nlm.nih.gov/pubmed/33424627
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fphys.2020.604580
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