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Monogenic autoinflammatory disorders: conceptual overview, phenotype, and clinical approach
Autoinflammatory diseases are conditions in which pathogenic inflammation arises primarily through antigen-independent hyperactivation of immune pathways. First recognized just over two decades ago, the autoinflammatory disease spectrum has expanded rapidly to include more than 40 distinct monogenic...
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| Publicat a: | J Allergy Clin Immunol |
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| Autors principals: | , , |
| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
2020
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC7727443/ https://ncbi.nlm.nih.gov/pubmed/33160483 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jaci.2020.08.017 |
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