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Dermatologic Manifestations of Monogenic Autoinflammatory Diseases

Autoinflammatory disorders are sterile inflammatory conditions characterized by episodes of early-onset fever, rash and disease-specific patterns of organ inflammation. Mutations in innate immune sensors that include the IL-1β activating inflammasomes, NLRP3, pyrin and NLRC4, pointed to the importan...

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Podrobná bibliografie
Vydáno v:Dermatol Clin
Hlavní autoři: Shwin, Kyawt Win, Lee, Chyi-Chia Richard, Goldbach-Mansky, Raphaela
Médium: Artigo
Jazyk:Inglês
Vydáno: 2017
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC5147585/
https://ncbi.nlm.nih.gov/pubmed/27890235
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.det.2016.07.005
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