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Monogenic autoinflammatory disorders: conceptual overview, phenotype, and clinical approach

Autoinflammatory diseases are conditions in which pathogenic inflammation arises primarily through antigen-independent hyperactivation of immune pathways. First recognized just over two decades ago, the autoinflammatory disease spectrum has expanded rapidly to include more than 40 distinct monogenic...

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Detalles Bibliográficos
Publicado en:J Allergy Clin Immunol
Main Authors: Nigrovic, Peter A., Lee, Pui Y., Hoffman, Hal M.
Formato: Artigo
Idioma:Inglês
Publicado: 2020
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC7727443/
https://ncbi.nlm.nih.gov/pubmed/33160483
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jaci.2020.08.017
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