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Extensive splicing changes in an ALS/FTD transgenic mouse model overexpressing cytoplasmic fused in sarcoma

Mutations in RNA-binding proteins (RBPs) such as TAR DNA-binding protein 43 (TDP-43) and fused in sarcoma (FUS) are associated with amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD). Recent evidence suggests that RNA dysregulation mediated by aberrant RBPs may play a critical rol...

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Detalhes bibliográficos
Publicado no:Sci Rep
Main Authors: Ito, Daisuke, Taguchi, Ryota, Deguchi, Maki, Ogasawara, Hideaki, Inoue, Eiji
Formato: Artigo
Idioma:Inglês
Publicado em: Nature Publishing Group UK 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7078223/
https://ncbi.nlm.nih.gov/pubmed/32184412
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-020-61676-x
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