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Polyglutamine-Expanded Androgen Receptor Alteration of Skeletal Muscle Homeostasis and Myonuclear Aggregation Are Affected by Sex, Age and Muscle Metabolism

Polyglutamine (polyQ) expansions in the androgen receptor (AR) gene cause spinal and bulbar muscular atrophy (SBMA), a neuromuscular disease characterized by lower motor neuron (MN) loss and skeletal muscle atrophy, with an unknown mechanism. We generated new mouse models of SBMA for constitutive an...

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Publicat a:Cells
Autors principals: Chivet, Mathilde, Marchioretti, Caterina, Pirazzini, Marco, Piol, Diana, Scaramuzzino, Chiara, Polanco, Maria Josè, Romanello, Vanina, Zuccaro, Emanuela, Parodi, Sara, D’Antonio, Maurizio, Rinaldi, Carlo, Sambataro, Fabio, Pegoraro, Elena, Soraru, Gianni, Pandey, Udai Bhan, Sandri, Marco, Basso, Manuela, Pennuto, Maria
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7072234/
https://ncbi.nlm.nih.gov/pubmed/32019272
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/cells9020325
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