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Immune dysregulation in patients with RAG deficiency and other forms of combined immune deficiency

Traditionally, primary immune deficiencies have been defined based on increased susceptibility to recurrent and/or severe infections. However, immune dysregulation, manifesting with autoimmunity or hyperinflammatory disease, has emerged as a common feature. This is especially true in patients affect...

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Dades bibliogràfiques
Publicat a:Blood
Autors principals: Delmonte, Ottavia M., Villa, Anna, Notarangelo, Luigi D.
Format: Artigo
Idioma:Inglês
Publicat: American Society of Hematology 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7046604/
https://ncbi.nlm.nih.gov/pubmed/31942628
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/blood.2019000923
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