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Inborn Errors of Immunity With Immune Dysregulation: From Bench to Bedside

Inborn errors of immunity are genetic disorders with broad clinical manifestations, ranging from increased susceptibility to infections to significant immune dysregulation, often leading to multiple autoimmune phenomena, lymphoproliferation, and malignancy. The treatment is challenging as it require...

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Podrobná bibliografie
Vydáno v:Front Pediatr
Hlavní autoři: Delmonte, Ottavia Maria, Castagnoli, Riccardo, Calzoni, Enrica, Notarangelo, Luigi Daniele
Médium: Artigo
Jazyk:Inglês
Vydáno: Frontiers Media S.A. 2019
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6718615/
https://ncbi.nlm.nih.gov/pubmed/31508401
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fped.2019.00353
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