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Changes in Airway Microbiome and Inflammation with Ivacaftor Treatment in Patients with Cystic Fibrosis and the G551D Mutation

Rationale: Modulation of the cystic fibrosis (CF) transmembrane conductance regulator (CFTR) protein improves clinical outcomes in patients with CF and specific CFTR genetic mutations. It remains unclear how improving CFTR function modifies existing airway infection and inflammation. Objectives: To...

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Dettagli Bibliografici
Pubblicato in:Ann Am Thorac Soc
Autori principali: Harris, J. Kirk, Wagner, Brandie D., Zemanick, Edith T., Robertson, Charles E., Stevens, Mark J., Heltshe, Sonya L., Rowe, Steven M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Thoracic Society 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6993801/
https://ncbi.nlm.nih.gov/pubmed/31604026
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1513/AnnalsATS.201907-493OC
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