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Neuronal network dysfunction precedes storage and neurodegeneration in a lysosomal storage disorder

Accumulation of lysosomal storage material and late-stage neurodegeneration are hallmarks of lysosomal storage disorders (LSDs) affecting the brain. Yet, for most LSDs, including CLN3 disease, the most common form of childhood dementia, it is unclear what mechanisms drive neurologic symptoms. Do def...

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Detalhes bibliográficos
Publicado no:JCI Insight
Main Authors: Ahrens-Nicklas, Rebecca C., Tecedor, Luis, Hall, Arron F., Lysenko, Elena, Cohen, Akiva S., Davidson, Beverly L., Marsh, Eric D.
Formato: Artigo
Idioma:Inglês
Publicado em: American Society for Clinical Investigation 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6948765/
https://ncbi.nlm.nih.gov/pubmed/31573978
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/jci.insight.131961
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