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Clarifying lysosomal storage diseases

Lysosomal storage diseases (LSDs) are a class of metabolic disorders caused by mutations in proteins critical for lysosomal function. Such proteins include lysosomal enzymes, lysosomal integral membrane proteins, and proteins involved in the post-translational modification and trafficking of lysosom...

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Autors principals: Schultz, Mark L, Tecedor, Luis, Chang, Michael, Davidson, Beverly L.
Format: Artigo
Idioma:Inglês
Publicat: 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3153126/
https://ncbi.nlm.nih.gov/pubmed/21723623
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.tins.2011.05.006
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