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RNA editing alterations define manifestation of prion diseases

Prion diseases are fatal neurodegenerative disorders caused by misfolding of the normal prion protein into an infectious cellular pathogen. Clinically characterized by rapidly progressive dementia and accounting for 85% of human prion disease cases, sporadic Creutzfeldt–Jakob disease (sCJD) is the p...

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Detaylı Bibliyografya
Yayımlandı:Proc Natl Acad Sci U S A
Asıl Yazarlar: Kanata, Eirini, Llorens, Franc, Dafou, Dimitra, Dimitriadis, Athanasios, Thüne, Katrin, Xanthopoulos, Konstantinos, Bekas, Nikolaos, Espinosa, Juan Carlos, Schmitz, Matthias, Marín-Moreno, Alba, Capece, Vincenzo, Shormoni, Orr, Andréoletti, Olivier, Bonn, Stefan, Torres, Juan María, Ferrer, Isidre, Zerr, Inga, Sklaviadis, Theodoros
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: National Academy of Sciences 2019
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC6765247/
https://ncbi.nlm.nih.gov/pubmed/31492812
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1803521116
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