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Lack of Huntingtin-Associated Protein-1 Causes Neuronal Death Resembling Hypothalamic Degeneration in Huntington's Disease

Huntington's disease (HD) is caused by a polyglutamine expansion in the disease protein huntingtin. The polyglutamine expansion causes huntingtin to interact abnormally with a number of proteins. However, it is unclear whether, and how, huntingtin-associated proteins are involved in the neurode...

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Detalhes bibliográficos
Publicado no:J Neurosci
Main Authors: Li, Shi-Hua, Yu, Zhao-Xue, Li, Cui-Lin, Nguyen, Huu-Phuc, Zhou, Yong-Xing, Deng, Chuxia, Li, Xiao-Jiang
Formato: Artigo
Idioma:Inglês
Publicado em: Society for Neuroscience 2003
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6740731/
https://ncbi.nlm.nih.gov/pubmed/12890790
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.23-17-06956.2003
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