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A More Efficient Conditional Mouse Model of Dravet Syndrome: Implications for Epigenetic Selection and Sex-Dependent Behaviors

BACKGROUND: Dravet Syndrome (DS) is an epileptic disorder characterized by spontaneous and thermally-induced seizures, hyperactivity, cognitive deficits, autistic-like behaviors, and Sudden Unexpected Death in Epilepsy (SUDEP). DS is caused by de novo loss-of-function mutations in the SCN1A gene. Se...

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Detalles Bibliográficos
Publicado en:J Neurosci Methods
Autores principales: Williams, Aaron D., Kalume, Franck, Westenbroek, Ruth E., Catterall, William A.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2019
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6686874/
https://ncbi.nlm.nih.gov/pubmed/31265868
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jneumeth.2019.108315
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