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Sirtuin signaling controls mitochondrial function in glycogen storage disease type Ia
Glycogen storage disease type Ia (GSD-Ia) deficient in glucose-6-phosphatase-α (G6Pase-α) is a metabolic disorder characterized by impaired glucose homeostasis and a long-term complication of hepatocellular adenoma/carcinoma (HCA/HCC). Mitochondrial dysfunction has been implicated in GSD-Ia but the...
Guardat en:
| Publicat a: | J Inherit Metab Dis |
|---|---|
| Autors principals: | , , , |
| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
2018
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6541525/ https://ncbi.nlm.nih.gov/pubmed/29740774 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10545-018-0192-1 |
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