Загрузка...
Sirtuin signaling controls mitochondrial function in glycogen storage disease type Ia
Glycogen storage disease type Ia (GSD-Ia) deficient in glucose-6-phosphatase-α (G6Pase-α) is a metabolic disorder characterized by impaired glucose homeostasis and a long-term complication of hepatocellular adenoma/carcinoma (HCA/HCC). Mitochondrial dysfunction has been implicated in GSD-Ia but the...
Сохранить в:
| Опубликовано в: : | J Inherit Metab Dis |
|---|---|
| Главные авторы: | , , , |
| Формат: | Artigo |
| Язык: | Inglês |
| Опубликовано: |
2018
|
| Предметы: | |
| Online-ссылка: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6541525/ https://ncbi.nlm.nih.gov/pubmed/29740774 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10545-018-0192-1 |
| Метки: |
Добавить метку
Нет меток, Требуется 1-ая метка записи!
|