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Dysregulated mitochondrial Ca(2+) and ROS signaling in skeletal muscle of ALS mouse model

Amyotrophic lateral sclerosis (ALS) is a devastating neuromuscular disease characterized by motor neuron loss and prominent skeletal muscle wasting. Despite more than one hundred years of research efforts, the pathogenic mechanisms underlying neuromuscular degeneration in ALS remain elusive. While t...

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Publicado en:Arch Biochem Biophys
Autores principales: Zhou, Jingsong, Li, Ang, Li, Xuejun, Yi, Jianxun
Formato: Artigo
Lenguaje:Inglês
Publicado: 2019
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6506190/
https://ncbi.nlm.nih.gov/pubmed/30682329
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.abb.2019.01.024
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