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Dysregulated mitochondrial Ca(2+) and ROS signaling in skeletal muscle of ALS mouse model

Amyotrophic lateral sclerosis (ALS) is a devastating neuromuscular disease characterized by motor neuron loss and prominent skeletal muscle wasting. Despite more than one hundred years of research efforts, the pathogenic mechanisms underlying neuromuscular degeneration in ALS remain elusive. While t...

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Dettagli Bibliografici
Pubblicato in:Arch Biochem Biophys
Autori principali: Zhou, Jingsong, Li, Ang, Li, Xuejun, Yi, Jianxun
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2019
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6506190/
https://ncbi.nlm.nih.gov/pubmed/30682329
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.abb.2019.01.024
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