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Hyperornithinemia‐hyperammonemia‐homocitrullinuria syndrome in pregnancy: Considerations for management and review of the literature

Hyperornithinemia‐hyperammonemia‐homocitrullinuria (HHH) syndrome is a rare metabolic autosomal recessive urea cycle disorder. Only about 100 patients have been reported in the literature. As the population survives into reproductive years, pregnancy management becomes a new challenge for this clini...

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Detaylı Bibliyografya
Yayımlandı:JIMD Rep
Asıl Yazarlar: Ho, Bernice, MacKenzie, Jennifer, Walia, Jagdeep, Geraghty, Michael, Smith, Graeme, Nedvidek, Julie, Guerin, Andrea
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: John Wiley & Sons, Inc. 2019
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC6498866/
https://ncbi.nlm.nih.gov/pubmed/31240152
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jmd2.12025
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