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Small molecule ion channels increase host defenses in cystic fibrosis airway epithelia

Loss-of-function mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) compromise epithelial HCO(3)(−) and Cl(−) secretion, reduce airway surface liquid (ASL) pH, and impair respiratory host defenses in people with cystic fibrosis (CF) (1–3). Here we report that apical addition...

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Dettagli Bibliografici
Pubblicato in:Nature
Autori principali: Muraglia, Katrina A., Chorghade, Rajeev S., Kim, Bo Ram, Tang, Xiao Xiao, Shah, Viral S., Grillo, Anthony S., Daniels, Page N., Cioffi, Alexander G., Karp, Philip H., Zhu, Lingyang, Welsh, Michael J., Burke, Martin D.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6492938/
https://ncbi.nlm.nih.gov/pubmed/30867598
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41586-019-1018-5
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