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Animal models for cystic fibrosis liver disease (CFLD)

Liver disease is a severe complication in patients with Cystic Fibrosis (CF), a genetic disease caused by mutations in the gene encoding for cystic fibrosis transmembrane conductance regulator (CFTR) channel. The sequence of events leading to CFLD is still unclear and has limited the development of...

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Détails bibliographiques
Publié dans:Biochim Biophys Acta Mol Basis Dis
Auteurs principaux: Fiorotto, Romina, Amenduni, Mariangela, Mariotti, Valeria, Cadamuro, Massimiliano, Fabris, Luca, Spirli, Carlo, Strazzabosco, Mario
Format: Artigo
Langue:Inglês
Publié: 2018
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC6474816/
https://ncbi.nlm.nih.gov/pubmed/30071276
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbadis.2018.07.026
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