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Animal models for cystic fibrosis liver disease (CFLD)

Liver disease is a severe complication in patients with Cystic Fibrosis (CF), a genetic disease caused by mutations in the gene encoding for cystic fibrosis transmembrane conductance regulator (CFTR) channel. The sequence of events leading to CFLD is still unclear and has limited the development of...

詳細記述

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書誌詳細
出版年:Biochim Biophys Acta Mol Basis Dis
主要な著者: Fiorotto, Romina, Amenduni, Mariangela, Mariotti, Valeria, Cadamuro, Massimiliano, Fabris, Luca, Spirli, Carlo, Strazzabosco, Mario
フォーマット: Artigo
言語:Inglês
出版事項: 2018
主題:
オンライン・アクセス:https://ncbi.nlm.nih.gov/pmc/articles/PMC6474816/
https://ncbi.nlm.nih.gov/pubmed/30071276
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbadis.2018.07.026
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