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The HCM-causing Y235S cMyBPC mutation accelerates contractile function by altering C1 domain structure

Mutations in cardiac myosin binding protein C (cMyBPC) are a major cause of hypertrophic cardiomyopathy (HCM). In particular, a single amino acid substitution of tyrosine to serine at residue 237 in humans (residue 235 in mice) has been linked to HCM with strong disease association. Although cMyBPC...

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Dades bibliogràfiques
Publicat a:Biochim Biophys Acta Mol Basis Dis
Autors principals: Doh, Chang Yoon, Li, Jiayang, Mamidi, Ranganath, Stelzer, Julian E.
Format: Artigo
Idioma:Inglês
Publicat: 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6434951/
https://ncbi.nlm.nih.gov/pubmed/30611859
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbadis.2019.01.007
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