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Disease-associated mutations of claudin-19 disrupt retinal neurogenesis and visual function

Mutations of claudin-19 cause Familial Hypomagnesaemia and Hypercalciuria, Nephrocalcinosis with Ocular Involvement. To study the ocular disease without the complications of the kidney disease, naturally occurring point mutations of human CLDN19 were recreated in human induced pluripotent cells or o...

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Dades bibliogràfiques
Publicat a:Commun Biol
Autors principals: Wang, Shao-Bin, Xu, Tao, Peng, Shaomin, Singh, Deepti, Ghiassi-Nejad, Maryam, Adelman, Ron A., Rizzolo, Lawrence J.
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group UK 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6433901/
https://ncbi.nlm.nih.gov/pubmed/30937396
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s42003-019-0355-0
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