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The ribonuclease PARN controls the levels of specific miRNAs that contribute to p53 regulation

PARN loss-of-function mutations cause a severe form of the hereditary disease dyskeratosis congenita (DC). PARN deficiency affects the stability of non-coding RNAs such as human telomerase RNA (hTR), but these effects do not explain the severe disease in patients. We demonstrate that PARN deficiency...

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Publicado en:Mol Cell
Autores principales: Shukla, Siddharth, Bjerke, Glen A., Muhlrad, Denise, Yi, Rui, Parker, Roy
Formato: Artigo
Lenguaje:Inglês
Publicado: 2019
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6430647/
https://ncbi.nlm.nih.gov/pubmed/30770239
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.molcel.2019.01.010
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