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A Human Skin Model Recapitulates Systemic Sclerosis Dermal Fibrosis and Identifies COL22A1 as a TGFβ Early Response Gene that Mediates Fibroblast to Myofibroblast Transition

Systemic sclerosis (SSc) is a complex multi-system autoimmune disease characterized by immune dysregulation, vasculopathy, and organ fibrosis. Skin fibrosis causes high morbidity and impaired quality of life in affected individuals. Animal models do not fully recapitulate the human disease. Thus, th...

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Detalhes bibliográficos
Publicado no:Genes (Basel)
Main Authors: Watanabe, Tomoya, Baker Frost, DeAnna, Mlakar, Logan, Heywood, Jonathan, da Silveira, Willian A., Hardiman, Gary, Feghali-Bostwick, Carol
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6409682/
https://ncbi.nlm.nih.gov/pubmed/30678304
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/genes10020075
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