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Unraveling obscurins in heart disease

Obscurins, expressed from the single OBSCN gene, are a family of giant, modular, cytoskeletal proteins that play key structural and regulatory roles in striated muscles. They were first implicated in the development of heart disease in 2007 when two missense mutations were found in a patient diagnos...

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Dettagli Bibliografici
Pubblicato in:Pflugers Arch
Autori principali: Grogan, Alyssa, Kontrogianni-Konstantopoulos, Aikaterini
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2018
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6397709/
https://ncbi.nlm.nih.gov/pubmed/30099631
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00424-018-2191-3
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