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Unraveling obscurins in heart disease

Obscurins, expressed from the single OBSCN gene, are a family of giant, modular, cytoskeletal proteins that play key structural and regulatory roles in striated muscles. They were first implicated in the development of heart disease in 2007 when two missense mutations were found in a patient diagnos...

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Dades bibliogràfiques
Publicat a:Pflugers Arch
Autors principals: Grogan, Alyssa, Kontrogianni-Konstantopoulos, Aikaterini
Format: Artigo
Idioma:Inglês
Publicat: 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6397709/
https://ncbi.nlm.nih.gov/pubmed/30099631
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00424-018-2191-3
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