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Unraveling obscurins in heart disease

Obscurins, expressed from the single OBSCN gene, are a family of giant, modular, cytoskeletal proteins that play key structural and regulatory roles in striated muscles. They were first implicated in the development of heart disease in 2007 when two missense mutations were found in a patient diagnos...

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Detalhes bibliográficos
Publicado no:Pflugers Arch
Main Authors: Grogan, Alyssa, Kontrogianni-Konstantopoulos, Aikaterini
Formato: Artigo
Idioma:Inglês
Publicado em: 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6397709/
https://ncbi.nlm.nih.gov/pubmed/30099631
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00424-018-2191-3
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