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Adenylyl cyclase 5 deficiency reduces renal cyclic AMP and cyst growth in an orthologous mouse model of polycystic kidney disease

Cyclic AMP promotes cyst growth in polycystic kidney disease (PKD) by stimulating cell proliferation and fluid secretion. Previously, we showed that the primary cilium of renal epithelial cells contains a cAMP regulatory complex comprising adenylyl cyclases 5 and 6 (AC5/6), polycystin-2, A-kinase an...

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Dades bibliogràfiques
Publicat a:Kidney Int
Autors principals: Wang, Qian, Cobo-Stark, Patricia, Patel, Vishal, Somlo, Stefan, Han, Pyung-Lim, Igarashi, Peter
Format: Artigo
Idioma:Inglês
Publicat: 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5794572/
https://ncbi.nlm.nih.gov/pubmed/29042084
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.kint.2017.08.005
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