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Adenylyl cyclase 5 deficiency reduces renal cyclic AMP and cyst growth in an orthologous mouse model of polycystic kidney disease

Cyclic AMP promotes cyst growth in polycystic kidney disease (PKD) by stimulating cell proliferation and fluid secretion. Previously, we showed that the primary cilium of renal epithelial cells contains a cAMP regulatory complex comprising adenylyl cyclases 5 and 6 (AC5/6), polycystin-2, A-kinase an...

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Detalles Bibliográficos
Publicado en:Kidney Int
Autores principales: Wang, Qian, Cobo-Stark, Patricia, Patel, Vishal, Somlo, Stefan, Han, Pyung-Lim, Igarashi, Peter
Formato: Artigo
Lenguaje:Inglês
Publicado: 2017
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5794572/
https://ncbi.nlm.nih.gov/pubmed/29042084
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.kint.2017.08.005
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