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Human copper transporter ATP7B (Wilson disease protein) forms stable dimers in vitro and in cells

ATP7B is a copper-transporting P(1B)-type ATPase (Cu-ATPase) with an essential role in human physiology. Mutations in ATP7B cause the potentially fatal Wilson disease, and changes in ATP7B expression are observed in several cancers. Despite its physiologic importance, the biochemical information abo...

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Pubblicato in:J Biol Chem
Autori principali: Jayakanthan, Samuel, Braiterman, Lelita T., Hasan, Nesrin M., Unger, Vinzenz M., Lutsenko, Svetlana
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Biochemistry and Molecular Biology 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5704462/
https://ncbi.nlm.nih.gov/pubmed/28842499
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M117.807263
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