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Dendritic Homeostasis Disruption in a Novel Frontotemporal Dementia Mouse Model Expressing Cytoplasmic Fused in Sarcoma

Cytoplasmic aggregation of fused in sarcoma (FUS) is detected in brain regions affected by amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD), which compose the disease spectrum, FUS proteinopathy. To understand the pathomechanism of ALS-FTD-associated FUS, we examined the behavio...

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Publicado en:EBioMedicine
Main Authors: Shiihashi, Gen, Ito, Daisuke, Arai, Itaru, Kobayashi, Yuki, Hayashi, Kanehiro, Otsuka, Shintaro, Nakajima, Kazunori, Yuzaki, Michisuke, Itohara, Shigeyoshi, Suzuki, Norihiro
Formato: Artigo
Idioma:Inglês
Publicado: Elsevier 2017
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5652009/
https://ncbi.nlm.nih.gov/pubmed/28928015
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ebiom.2017.09.005
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