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MicroRNA-9 downregulates the ANO1 chloride channel and contributes to cystic fibrosis lung pathology

Cystic fibrosis results from reduced cystic fibrosis transmembrane conductance regulator protein activity leading to defective epithelial ion transport. Ca(2+)-activated Cl(−) channels mediate physiological functions independently of cystic fibrosis transmembrane conductance regulator. Anoctamin 1 (...

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Publicat a:Nat Commun
Autors principals: Sonneville, Florence, Ruffin, Manon, Coraux, Christelle, Rousselet, Nathalie, Le Rouzic, Philippe, Blouquit-Laye, Sabine, Corvol, Harriet, Tabary, Olivier
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group UK 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5617894/
https://ncbi.nlm.nih.gov/pubmed/28955034
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41467-017-00813-z
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